Epithelioid Hemangioendothelioma: A Case with Large Solitary Pulmonary Mass and Hypertrophic Osteoarthropathy


1 Department of Respiratory Medicine,

2 Department of Pathology, Imam-Khomeini Hospital, Urmia University of Medical Sciences and Health Services, URMIA- IRAN


We describe a case of pulmonary epithelioid hemangioendothelioma (PEH), previously known as intravascular bronchoalveolar tumor, in a 48- year-old woman with an initial diagnosis made by CT-guided transthoracic needle biopsy. This is a rare disease, with approximately 50 cases described in the literature. To our knowledge, this has not been previously described in the English-language literature. This tumor can affect multiple organs. PEH is usually multifocal or small sized; hypertrophic osteoarthropathy is uncommon. This patient presented with hypertrophic osteoarthropathy and large solitary pulmonary mass, rare presentations of this uncommon tumor.(Tanaffos 2005; 4(16): 73-78)