A 38-Year-Old Woman with Scimitar Syndrome


1 Department of Internal Medicine, Pulmonary and Critical Care Division,

2 Department of Radiology, Mazandaran University of Medical Sciences, Sari, Iran.


Scimitar syndrome is a rare clinical syndrome which consists of anomalous right pulmonary venous return to the inferior vena cava. Scimitar syndrome classically involves the right lung and is most commonly reported in very early infancy. However, it is occasionally seen in adults. We present a 38 year-old woman complaining of dry cough and exertional dyspnea during moderate exercise with right lung scimitar syndrome. The chest radiography showed increased radiolucency of the left lung and heart dextroposition with a characteristic appearance of scimitar sign which is a curvilinear density in the right middle and lower pulmonary fields resembling a curved Turkish sword. (Tanaffos2011; 10(3): 63-66)