Pleuropulmonary Blastoma: Case Report

Authors

1 Department of Pathology, Mashhad University of Medical Sciences and Health Services,

2 Department of Pathology, NRITLD, Shaheed Beheshti University of Medical Sciences and Health Services, MASHHAD-IRAN.

3 Department of Pathology, Mashhad University of Medical Sciences and Health Services

Abstract

Pleuropulmonary blastoma (PPB) is a rare and aggressive tumor that is emerging as a distinct entity of childhood disease .It is characterized by mesenchymal elements (including undifferentiated blastoma and often cartilaginous, rhabdomyoblastic, or fibroblastic differentiation) and epithelium-lined spaces. PPB may be exclusively cystic (type I), solid (type III) or both solid and cystic (type II). A 5-month-old boy presented with a history of fever and respiratory distress. Chest radiograph and subsequent CT scan showed a large soft-tissue density occupying the left chest cavity. Radical resection of the mass was achieved by lobectomy. Histologic examination revealed PPB (type II). (Tanaffos 2004; 3(11): 71-76)

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