Lung Transplantation Research Center, National Research Institute of Tuberculosis and Lung Diseases (NRITLD), Shahid Beheshti University of Medical Sciences, Tehran, Iran,
Chronic Respiratory Diseases Research Center, (NRITLD), Shahid Beheshti University of Medical Sciences, Tehran, Iran.
Department of Pulmonary Medicine, Iran University of Medical Sciences, Tehran, Iran.
Unilateral pulmonary artery agenesis (UPAA) is an uncommon congenital anomaly and most patients present in neonatal period with respiratory symptoms. Left-sided pulmonary artery agenesis is less frequent than rightsided and is sometimes associated with cardiac anomalies. We report a patient with a history of repaired ventricular septal defect, who presented with cough and hemoptysis and the diagnosis of UPAA was made.