TY - JOUR ID - 243021 TI - Anesthesia Management of Vitrectomy in a Patient with Sturge-Weber Syndrome JO - TANAFFOS (Respiration) JA - RSPR LA - en SN - 1735-0344 AU - Roodneshin, Fatemeh AU - Poor Zamany Nejat Kermany, Mahtab AU - Rostami, Pooya AU - Tanghatari, Hamed AD - Labbafinejad Medical Center, Department of Anesthesiology, Shahid Beheshti University of Medical Sciences, Tehran, Iran AD - Department of Anesthesiology, Shahid Beheshti University of Medical Sciences, Tehran, Iran. Y1 - 2018 PY - 2018 VL - 17 IS - 1 SP - 57 EP - 61 KW - Sturge-Weber syndrome KW - Propofol KW - Difficult airway DO - N2 - Sturge-Weber syndrome (SWS) is a neurocutaneous disorder, characterized by leptomeningeal angiomas involving the oral cavity, trachea, larynx, and face. Herein, we present a case of vitrectomy in a seven-year-old boy with SWS. The patient showed hemangioma on the left side of his face, as well as mental retardation and epilepsy. Preoperative examination revealed no apparent hemangioma in the oral cavity, pharynx, larynx, or trachea. However, he was predicted to have difficult airway intubation, as the oral cavity was smaller than the normal size. The minimum Mallampati score was 3-4 due to macroglossia. First, we applied awake intubation, but he failed to follow the commands. We proceeded to general anesthesia with propofol and did not use any muscle relaxants to maintain spontaneous breathing. A laryngeal mask airway was inserted to minimize any harm to possible oral angiomas. The patient was hemodynamically stable and extubated without any complications, such as bleeding or respiratory problems. UR - https://www.tanaffosjournal.ir/article_243021.html L1 - https://www.tanaffosjournal.ir/article_243021_51bcbd4a94be29f22c31ddde18763ba8.pdf ER -