Department of Internal Medicine, Kashan University of Medical Sciences, KASHAN- IRAN.
Pulmonary involvement in tuberous sclerosis is very rare and seems to be associated with a more benign course. We present a 21-year-old woman with bilateral angiomyolipoma. She developed spontaneous pneumothorax which was successfully managed by tube thoracostomy. No recurrence of pneumothorax has been observed up to the present (4 years follow-up). (Tanaffos 2009; 8(2): 64-68)